Granulomatosis linfomatoide
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Transcript of Granulomatosis linfomatoide
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CITOLOGIA EN LA GRANULOMATOSIS LINFOMATIDE
http://www.garciaureta.com/
A PROPOSITO DE UN CASO
Ernesto Garcia-Ureta
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Varón 82 años
Gran Masa
Hiliar Izq.
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Fondo Hemorragico
Restos Necroticos
Escasa Celularidad
Celularidad Linfoide
Linfocitos Pequeños
Ocasionales Células Linfoides Grandes
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LC
LC
CD-10
CD-10
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CD-3
CD-3
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CD-79
CD-79
CD-20
CD-20
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CD-30
CD-30
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CD-20 CD-79 CD-3 CD-5 Cd-30 EBER
C. GRANDES + + + + 50%
C. PEQUEÑAS + +
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Pulmón, el más frecuente 97%.
Piel.
Riñón.
Hígado.
Sistema nervioso central 30%.
> 5% son asintomáticos.
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Nódulos pulmonares de variable tamaño.
Adenopatías mediastínicas.
Derrame pleural.
Neumotórax.
Neumomediastino.
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Células B CD-20 positivas, grandes, atípicas.
- Linfocitos.
- Plasmáticas.
- Histiocitos.
Numerosas células T CD-3 positivas.
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TIPO I 1 – 5%
TIPO II 5 - 50 %
TIPO III + 50 %
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GRADO 1…………..1/3…………………Linfoma
GRADO 2…………..2/3…………………Linfoma
GRADO 3……………..…………………..Linfoma
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Katzenstein AL
Mod Pathol. 1990; 3:435-41.
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Proceso linfoproliferativo de células B rico en células T.
Asociado al virus Epstein-Barr.
5ª- 6ª década de la vida.
Estados inmunosupresión e inmunodeficiencia.
2 veces más frecuente en hombres que en mujeres.
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Liebow AA
Hum Pathol. 1972; 3: 457-558.
Katzenstein AL
Mod Pathol. 1990; 3: 435-41
Lundell RB
Cancer Treat Res. 2008;142: 265-72.
Alinari L
Head Neck Pathol. 2012; 6:496-501.
Roschewski M
Cancer J. 2012;18: 469-74.
Mohyuddin GR
Case Rep Pulmonol. 2012; 2012: 371490.
Ammannagari N
Ann Hematol. 2013; 92: 981-3.
Tagliavini E
Pathologica. 2013; 105: 111-6.
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Ernesto Garcia-Ureta